Caroli’s disease is a rare congenital disorder characterized by multiple segmental cystic dilatations of the intra-hepatic bile ducts that are related to each other. Caroli’s syndrome is more common and associated with hepatic fibrosis and renal cystic disease. This paper introduces a three year old boy with Caroli’s disease and medullary nephrocalcinosis presented with fever, abdominal pain, and anorexia.

  SOURCE: URMIA MED J 2013: 24(9): 744 ISSN: 1027-3727